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Motor Neuron Disorders Edited by Pamela J. Shaw, M.B.B.S., M.D., F.R.C.P. Head of Academic Neurology Unit and Professor of Neurology, University of Sheffield; Consultant Neurologist, Royal Hallamshire Hospital, Sheffield, United Kingdom and Michael J. Strong, M.D., F.R.C.P.C. Professor and Co-chair, Department of Clinical Neurological Sciences, Arthur Hudson Chair in ALS Research, The University of Western Ontario; Cell Biology Research Group, Robarts Research Institute, London, Ontario, Canada An Imprint of Elsevier Science